Best Cases: Congenital Heart Disease-Evolution of Double-chambered Left Ventricle

Evolution of Double-chambered Left Ventricle

Video Transcription

Video Summary

A former 31-week premature boy developed a double-chambered left ventricle that evolved over time. As a newborn, echocardiography showed a normal heart with a membrane crossing the LV but unobstructed flow. By age 4, the membrane had thickened, nearly dividing the LV and causing LV hypertrophy. MRI showed poor apical chamber function, sluggish flow, and late gadolinium enhancement of the band and apical endocardium. Catheterization confirmed higher apical pressure and near stasis of contrast. The case illustrates progressive, unusual double-chambered LV anatomy, with surgery being considered because of obstruction and tissue changes.

Keywords

double-chambered left ventricle

premature infant

left ventricular hypertrophy

cardiac MRI

left ventricular obstruction