Case Session 02: Non-ischemic Cardiomyopathies (2018)-Right ventricular outflow tract obstruction in the setting of hypertrophic cardiomyopathy

Right ventricular outflow tract obstruction in the setting of hypertrophic cardiomyopathy

Video Transcription

Video Summary

The speaker presents a case of right ventricular outflow tract obstruction in a 42-year-old woman evaluated by cardiac MRI after an inconclusive echocardiogram for a murmur. Imaging showed marked asymmetric septal hypertrophy, right ventricular free-wall thickening, possible apical aneurysm, fibrosis, and dynamic RVOT obstruction with a 30 mmHg gradient. The main diagnostic challenge was determining whether obstruction was due to hypertrophied crista superventricularis or septal tissue; the speaker favors septal hypertrophy as the main cause. The case highlights that patients with hypertrophic cardiomyopathy can also have clinically important right ventricular abnormalities.

Keywords

right ventricular outflow tract obstruction

hypertrophic cardiomyopathy

cardiac MRI

septal hypertrophy

right ventricular abnormalities