Pediatric and Congenital Heart Disease Session 5: Does CMR Impact the Management of Ebstein's Anomaly?-Congenital Tricuspid Valve Lesions: Is It Ebstein Anomaly ?

Congenital Tricuspid Valve Lesions: Is It Ebstein Anomaly ?

Video Transcription

Video Summary

The transcript explains Ebstein anomaly of the tricuspid valve: failure of leaflet delamination causes the septal and posterior leaflets to be displaced into the right ventricle, while the anterior leaflet becomes large, curtain-like, and tethered to the RV free wall or septal structures. This creates an atrialized portion of the right ventricle, often with global thinning and abnormal chordae, and can cause arrhythmias and tricuspid regurgitation. Related conditions include Uhl anomaly, pulmonary atresia with intact septum, and left-sided Ebstein anomaly in transposition. It also contrasts true Ebstein with myxomatous dysplastic tricuspid valve disease.

Keywords

Ebstein anomaly

tricuspid valve

atrialized right ventricle

tricuspid regurgitation

congenital heart disease