Technologist Track Session 3: How I Do It: Patients with Cardiomyopathies-Arrhythmogenic Right Ventricular Cardiomyopathy

Video Transcription

Video Summary

The talk reviewed arrhythmogenic right ventricular cardiomyopathy (ARVC), a rare but important genetic disease because it can cause sudden cardiac death. Diagnosis relies on task force criteria combining imaging, electrical findings, family history, and genetics. On CMR, ARVC requires both qualitative RV wall-motion abnormalities and quantitative abnormalities such as reduced RVEF or increased RV volume. The most important scan is high-quality cine SSFP imaging in short-axis and axial planes, especially for careful RV quantification. LGE and T2 imaging are recommended to assess mimics like myocarditis and sarcoidosis, and to evaluate possible left-sided arrhythmogenic cardiomyopathy. Fat imaging and T1 mapping are optional and not central to diagnosis. The speaker emphasized common pitfalls, including pectus deformity, RV tethering, and overcalling fat infiltration or isolated abnormalities that do not meet criteria.

Keywords

arrhythmogenic right ventricular cardiomyopathy

ARVC diagnosis

cardiac MRI

right ventricular abnormalities

sudden cardiac death